SOFT TISSUE ROSAI: DORFMAN DISEASE OF THE SACRAL REGION, A VERY RARE DISEASE: CASE REPORT AND REVIEW OF LITERATURE

CORRESPONDING AUTHOR:
Dr. Jomine Jose,
Associate Professor,
Department of General Surgery,
MOSC Medical College,
Kolenchery,
Ernakulam-682311.
Email: jomine9@gmail.com

ABSTRACT: INTRODUCTION: Rosai–Dorfman disease (RDD) is a rare proliferative histiocytic disorder of unknown etiology. RDD typically presents with generalized lymphadenopathy and polymorphic histiocytic infiltration of the lymph node sinuses; however, occurrences of extranodal soft tissue RDD may rarely occur. We are presenting a case that presented as a subcutaneous swelling. CONCLUSION: RDD is a rare inflammatory lesion that should be considered in the differential diagnosis of a soft tissue tumor. Differentiation of extra nodal RDD from more common soft tissue tumors such as soft tissue sarcoma or inflammatory my fibroblastic tumor is difficult and usually requires definitive surgical excision with histopathological examination. The optimal treatment for extra nodal RDD is surgical excision and is usually curative.

KEYWORDS: Rosai Dorfman, soft tissue swelling.